{"id":7880,"date":"2020-02-20T15:13:54","date_gmt":"2020-02-20T13:13:54","guid":{"rendered":"https:\/\/havas.cz\/?post_type=pressroom&#038;p=7880"},"modified":"2020-10-14T10:20:09","modified_gmt":"2020-10-14T08:20:09","slug":"imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni","status":"publish","type":"pressroom","link":"https:\/\/havas.cz\/en\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/","title":{"rendered":"Imunitn\u00ed trombocytopenick\u00e1 purpura je nen\u00e1padn\u00e9, ale zr\u00e1dn\u00e9 hematologick\u00e9 onemocn\u011bn\u00ed"},"content":{"rendered":"<p>Imunitn\u00ed trombocytopenick\u00e1 purpura, pro ni\u017e je tak\u00e9 \u010dasto pou\u017e\u00edv\u00e1n v\u00fdraz imunitn\u00ed trombocytopenie, je autoimunitn\u00ed onemocn\u011bn\u00ed, kter\u00e9 l\u00e9ka\u0159i ro\u010dn\u011b diagnostikuj\u00ed asi 70 a\u017e 100 nov\u00fdm pacient\u016fm na jeden milion obyvatel. Z&nbsp;toho polovina jsou d\u011bti mlad\u0161\u00ed 15 let. U&nbsp;dosp\u011bl\u00fdch je nej\u010dast\u011bj\u0161\u00ed ve v\u011bku 18\u201340 let, zhruba t\u0159ikr\u00e1t \u010dast\u011bj\u0161\u00ed je pak u&nbsp;\u017een ne\u017e u&nbsp;mu\u017e\u016f. Jedn\u00e1 se o&nbsp;onemocn\u011bn\u00ed, je\u017e b\u00fdv\u00e1 v\u00a080\u00a0% prim\u00e1rn\u00ed,<sup>3,4<\/sup> kdy p\u0159\u00ed\u010diny jsou r\u016fznorod\u00e9. \u010casto m\u016f\u017ee propuknout po b\u011b\u017en\u00fdch (nespecifick\u00fdch) vir\u00f3z\u00e1ch d\u00fdchac\u00edho \u010di za\u017e\u00edvac\u00edho traktu nebo ve spojen\u00ed s&nbsp;jin\u00fdmi nemocemi, nap\u0159\u00edklad mononukle\u00f3zou.<sup>3<\/sup> Ve 20\u00a0% p\u0159\u00edpad\u016f m\u016f\u017ee b\u00fdt jeho vznik spojen nap\u0159\u00edklad s&nbsp;u\u017e\u00edv\u00e1n\u00edm n\u011bkter\u00fdch l\u00e9k\u016f, o\u010dkov\u00e1n\u00edm, n\u00e1dorov\u00fdm onemocn\u011bn\u00edm, infekc\u00ed, jako je nap\u0159\u00edklad HIV nebo hepatitida B, jin\u00fdm imunitn\u00edm onemocn\u011bn\u00edm nebo poruchami funkce sleziny.<sup>3,4<\/sup><\/p>\n<p><em>\u201eN\u00e1zev imunitn\u00ed trombocytopenick\u00e1 purpura si onemocn\u011bn\u00ed vyslou\u017eilo kv\u016fli krv\u00e1cen\u00ed do k\u016f\u017ee s\u00a0tvorbou petechi\u00ed \u2013 drobn\u00fdch te\u010dkovit\u00fdch krv\u00e1cen\u00ed a&nbsp;mod\u0159in. D\u00e1le doch\u00e1z\u00ed ke krv\u00e1cen\u00ed v\u00a0oblasti dutiny \u00fastn\u00ed, z&nbsp;nosu, \u017eeny a&nbsp;d\u00edvky mohou m\u00edt silnou menstruaci. Vz\u00e1cn\u011b pacienti krv\u00e1cej\u00ed do za\u017e\u00edvac\u00edho \u010di mo\u010dov\u00e9ho traktu, v\u00fdjime\u010dn\u011b i&nbsp;centr\u00e1ln\u00ed nervov\u00e9 soustavy \u2013 mozku. Krv\u00e1civ\u00e9 projevy by pacienti \u010di jejich rodi\u010de nem\u011bli podce\u0148ovat a&nbsp;m\u011bli by se nechat v\u010das vy\u0161et\u0159it l\u00e9ka\u0159em,\u201c<sup>5<\/sup> <\/em>objas\u0148uje MUDr. Veronika Fiamoli, Ph.D., z\u00a0Odd\u011blen\u00ed d\u011btsk\u00e9 hematologie Fakultn\u00ed nemocnice Brno.<\/p>\n<p><strong>Co se d\u011bje s\u00a0imunitn\u00edm syst\u00e9mem<\/strong><\/p>\n<p>Imunitn\u00ed trombocytopenick\u00e1 purpura je v\u00a0podstat\u011b porucha imunity, kdy vlastn\u00ed imunitn\u00ed syst\u00e9m po\u0161kozuje synchronizovan\u00fd proces zdrav\u00ed. Organismus za\u010dne komplexn\u011b ni\u010dit vlastn\u00ed krevn\u00ed desti\u010dky neboli trombocyty. Rovn\u011b\u017e pak utlumuje tvorbu z\u00e1rode\u010dn\u00fdch bun\u011bk krevn\u00edch desti\u010dek. Pro p\u0159esn\u011bj\u0161\u00ed vysv\u011btlen\u00ed: imunitn\u00ed syst\u00e9m v\u00a0kostn\u00ed d\u0159eni napad\u00e1 z\u00e1rode\u010dn\u00e9 bu\u0148ky krevn\u00edch desti\u010dek je\u0161t\u011b d\u0159\u00edve, ne\u017e stihnou dozr\u00e1t a&nbsp;dostat se do krevn\u00edho ob\u011bhu. Dopad t\u00e9to poruchy na zdrav\u00ed \u010dlov\u011bka je v\u00fdznamn\u00fd, nebo\u0165 krevn\u00ed desti\u010dky pln\u00ed v&nbsp;na\u0161\u00ed krvi nepostradatelnou \u00falohu. D\u00edky sv\u00e9 schopnosti p\u0159ilnout k&nbsp;poran\u011bn\u00e9 c\u00e9v\u011b, shlukovat se a\u00a0m\u011bnit tvar dok\u00e1\u017e\u00ed ve spolupr\u00e1ci s&nbsp;dal\u0161\u00edmi l\u00e1tkami v&nbsp;krevn\u00ed plazm\u011b vytvo\u0159it krevn\u00ed sra\u017eeninu, kter\u00e1 ucpe po\u0161kozenou st\u011bnu c\u00e9vy, \u010d\u00edm\u017e zastav\u00ed krv\u00e1cen\u00ed. A\u010d si to m\u00e1lokdo uv\u011bdomuje, maj\u00ed funkci nejide\u00e1ln\u011bj\u0161\u00edch n\u00e1plast\u00ed.<sup>3<\/sup><\/p>\n<p><strong>Jak\u00e9 jsou mo\u017enosti l\u00e9\u010dby<\/strong><\/p>\n<p>Stejn\u011b tak jako u&nbsp;velk\u00e9 \u0159ady jin\u00fdch onemocn\u011bn\u00ed krve maj\u00ed specialist\u00e9 mo\u017enosti l\u00e9\u010dby i&nbsp;v\u00a0p\u0159\u00edpad\u011b t\u00e9to nemoci. Pokud pacient trp\u00ed podez\u0159el\u00fdmi projevy, nap\u0159\u00edklad pr\u00e1v\u011b mod\u0159inami, l\u00e9ka\u0159 ho po\u0161le na laboratorn\u00ed vy\u0161et\u0159en\u00ed krevn\u00edho obrazu, kter\u00e9 ur\u010d\u00ed mimo jin\u00e9 i&nbsp;po\u010det krevn\u00edch desti\u010dek. V\u00a0p\u0159\u00edpad\u011b, \u017ee se prok\u00e1\u017ee sn\u00ed\u017een\u00ed po\u010dtu desti\u010dek, je nutn\u00e9 zah\u00e1jit l\u00e9\u010dbu. N\u00e1sleduj\u00edc\u00ed terapie m\u00e1 n\u011bkolik lini\u00ed. V\u00a0prvn\u00ed m\u016f\u017ee l\u00e9ka\u0159 nasadit kortikosteroidy nebo imunoglobuliny. Druh\u00e1 linie se t\u00fdk\u00e1 pod\u00e1v\u00e1n\u00ed l\u00e9k\u016f, kter\u00e9 podporuj\u00ed tvorbu krevn\u00edch desti\u010dek v\u00a0kostn\u00ed d\u0159eni nebo imunosupresiv neboli l\u00e9k\u016f potla\u010duj\u00edc\u00edch imunitu. Pouze v\u00a0nejnutn\u011bj\u0161\u00edch p\u0159\u00edpadech l\u00e9ka\u0159 zvol\u00ed chirurgick\u00e9 odstran\u011bn\u00ed sleziny.<sup>3,6<\/sup> \u201e<em>Velk\u00e9 pokroky v\u00a0medic\u00edn\u011b p\u0159inesly v\u00a0posledn\u00edch letech pro pacienty s\u00a0imunitn\u00ed trombocytopenickou purpurou nov\u00e9 l\u00e9\u010debn\u00e9 mo\u017enosti. Nicm\u00e9n\u011b d\u016fraz je p\u0159edev\u0161\u00edm kladen na individu\u00e1ln\u00ed posouzen\u00ed ka\u017ed\u00e9ho pacienta a&nbsp;volbu l\u00e9\u010debn\u00e9ho postupu,<\/em> <em>kter\u00fd je pro n\u011bj nejefektivn\u011bj\u0161\u00ed a&nbsp;umo\u017e\u0148uje mu \u017e\u00edt s&nbsp;co nejmen\u0161\u00edmi omezen\u00edmi,<\/em>\u201c<sup>7<\/sup> dopl\u0148uje MUDr. Veronika Fiamoli, Ph.D.<\/p>\n<p>Krev je tekutinou na\u0161eho \u017eivota. Krevn\u00ed elementy, kter\u00e9 jsou jej\u00ed nezbytnou sou\u010d\u00e1st\u00ed, nesm\u00ed chyb\u011bt, ale ani p\u0159eb\u00fdvat. Jedin\u011b tak m\u016f\u017ee t\u00e9ct spr\u00e1vn\u00fdm tempem, tak jak m\u00e1 \u2013 ani p\u0159\u00edli\u0161 rychle, ani pomalu \u2013 a&nbsp;plnit v\u0161echny sv\u00e9 d\u016fle\u017eit\u00e9 funkce. I&nbsp;krev m\u016f\u017ee b\u00fdt nemocn\u00e1 a\u00a0stejn\u011b tak jako u&nbsp;\u0159ady jin\u00fdch onemocn\u011bn\u00ed je pro \u00fasp\u011b\u0161n\u00e9 zvl\u00e1dnut\u00ed choroby nutn\u00fd aktivn\u00ed p\u0159\u00edstup pacienta, kter\u00fd nav\u0161t\u00edv\u00ed l\u00e9ka\u0159e v\u010das.<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Kontakt pro m\u00e9dia: <\/strong><\/p>\n<p>Mark\u00e9ta Stillerov\u00e1, Senior PR Manager, Havas, 702\u00a0213\u00a0341, <a href=\"mailto:marketa.stillerova@havaspr.com\">marketa.stillerova@havaspr.com<\/a><\/p>\n<p>Michaela Jura\u010d\u00e1kov\u00e1, PR Executive, Havas, 602\u00a0766&nbsp;398, <a href=\"mailto:michaela.juracakova@havaspr.com\">michaela.juracakova@havaspr.com<\/a><\/p>\n<p><strong>Zdroje:<\/strong><\/p>\n<ol>\n<li>\u00daHKT. D\u00e1rci krve. (online). Dostupn\u00e9 z: <a href=\"https:\/\/www.uhkt.cz\/darci\/darovani-krve\/sub_article_16\">https:\/\/www.uhkt.cz\/darci\/darovani-krve\/sub_article_16<\/a><\/li>\n<li>Bylo v\u00e1m diagnostikov\u00e1no onemocn\u011bn\u00ed zvan\u00e9 ITP? (online). Dostupn\u00e9 z: <a href=\"http:\/\/www.trombocytopenie.cz\/bylo-vam-diagnostikovano-onemocneni-zvane-itp\/\">http:\/\/www.trombocytopenie.cz\/bylo-vam-diagnostikovano-onemocneni-zvane-itp\/<\/a><\/li>\n<li>KOZ\u00c1K Tom\u00e1\u0161. Prim\u00e1rn\u00ed imunitn\u00ed trombocytopenie (ITP). Informace pro pacienty a&nbsp;jejich bl\u00edzk\u00e9. (online). Dostupn\u00e9 z: <a href=\"http:\/\/trombocytopenie.cz\/wp-content\/uploads\/2016\/01\/ITP_brozura.pdf\">http:\/\/trombocytopenie.cz\/wp-content\/uploads\/2016\/01\/ITP_brozura.pdf<\/a><\/li>\n<li>KOZ\u00c1K Tom\u00e1\u0161. Imunitn\u00ed trombocytopenick\u00e1 purpura u&nbsp;dosp\u011bl\u00fdch. (online). Dostupn\u00e9 z: <a href=\"http:\/\/www.trombocytopenie.cz\/imunitni-trombocytopenicka-purpura-itp-u-dospelych\/\">http:\/\/www.trombocytopenie.cz\/imunitni-trombocytopenicka-purpura-itp-u-dospelych\/<\/a><\/li>\n<li>Nebezpe\u010d\u00ed spo\u010d\u00edv\u00e1 v&nbsp;p\u0159ehl\u00ed\u017een\u00ed p\u0159\u00edznak\u016f. (online). Dostupn\u00e9 z: <a href=\"http:\/\/www.trombocytopenie.cz\/trombocytopenie-nebezpeci-spociva-v-prehlizeni-priznaku\/\">http:\/\/www.trombocytopenie.cz\/trombocytopenie-nebezpeci-spociva-v-prehlizeni-priznaku\/<\/a><\/li>\n<li>Doporu\u010den\u00ed \u010cHS pro diagnostiku a&nbsp;l\u00e9\u010dbu imunitn\u00ed trombocytopenie (ITP). Koz\u00e1k T., \u010cerm\u00e1k J., \u010cervinek L. a\u00a0kol. Transfuze a&nbsp;hematologie dnes 2017<\/li>\n<li>Nebezpe\u010dn\u00e1 porucha sr\u00e1\u017elivosti krve: Trombocytopenie. (online). Dostupn\u00e9 z: <a href=\"http:\/\/www.trombocytopenie.cz\/nebezpecna-porucha-srazlivosti-krve-trombocytopenie\/\">http:\/\/www.trombocytopenie.cz\/nebezpecna-porucha-srazlivosti-krve-trombocytopenie\/<\/a><\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>Krev se v lidsk\u00e9m t\u011ble vym\u011bn\u00ed ka\u017ed\u00e9 t\u0159i, \u010dty\u0159i m\u011bs\u00edce, ani\u017e bychom si toho v\u016fbec v\u0161imli.<sup>1<\/sup> P\u0159itom dod\u00e1v\u00e1 organismu l\u00e1tky, bez kter\u00fdch by \u017eivot nebyl mo\u017en\u00fd. Tak jako je rozmanit\u00e1 krev, jsou rozmanit\u00e1 i krevn\u00ed onemocn\u011bn\u00ed. N\u00e1v\u0161t\u011bva hematologie nemus\u00ed ale rozhodn\u011b znamenat pouze onemocn\u011bn\u00ed leukemi\u00ed, a\u010dkoli i s jej\u00ed l\u00e9\u010dbou medic\u00edna velmi pokro\u010dila. Mezi m\u00e9n\u011b zn\u00e1m\u00e1 krevn\u00ed onemocn\u011bn\u00ed pat\u0159\u00ed imunitn\u00ed trombocytopenick\u00e1 purpura. Ta se zpo\u010d\u00e1tku m\u016f\u017ee projevovat jen zv\u00fd\u0161enou tvorbou mod\u0159in, krv\u00e1cen\u00edm z nosu nebo d\u00e1sn\u00ed. Projevy onemocn\u011bn\u00ed jsou zap\u0159\u00ed\u010din\u011bn\u00e9 reakc\u00ed imunitn\u00edho syst\u00e9mu, kter\u00fd postupn\u011b ni\u010d\u00ed krevn\u00ed desti\u010dky, co\u017e m\u00e1 za n\u00e1sledek zv\u00fd\u0161en\u00e9 riziko krv\u00e1cen\u00ed.<sup>2<\/sup> <\/p>\n","protected":false},"author":48,"featured_media":0,"menu_order":0,"template":"","meta":{"_links_to":"","_links_to_target":""},"pressroom_category":[],"pressroom_tag":[204],"class_list":["post-7880","pressroom","type-pressroom","status-publish","hentry","pressroom_tag-zdravi"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Imunitn\u00ed trombocytopenick\u00e1 purpura je nen\u00e1padn\u00e9, ale zr\u00e1dn\u00e9 hematologick\u00e9 onemocn\u011bn\u00ed - Havas Prague<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/havas.cz\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Imunitn\u00ed trombocytopenick\u00e1 purpura je nen\u00e1padn\u00e9, ale zr\u00e1dn\u00e9 hematologick\u00e9 onemocn\u011bn\u00ed - Havas Prague\" \/>\n<meta property=\"og:description\" content=\"Krev se v lidsk\u00e9m t\u011ble vym\u011bn\u00ed ka\u017ed\u00e9 t\u0159i, \u010dty\u0159i m\u011bs\u00edce, ani\u017e bychom si toho v\u016fbec v\u0161imli.1 P\u0159itom dod\u00e1v\u00e1 organismu l\u00e1tky, bez kter\u00fdch by \u017eivot nebyl mo\u017en\u00fd. Tak jako je rozmanit\u00e1 krev, jsou rozmanit\u00e1 i krevn\u00ed onemocn\u011bn\u00ed. N\u00e1v\u0161t\u011bva hematologie nemus\u00ed ale rozhodn\u011b znamenat pouze onemocn\u011bn\u00ed leukemi\u00ed, a\u010dkoli i s jej\u00ed l\u00e9\u010dbou medic\u00edna velmi pokro\u010dila. Mezi m\u00e9n\u011b zn\u00e1m\u00e1 krevn\u00ed onemocn\u011bn\u00ed pat\u0159\u00ed imunitn\u00ed trombocytopenick\u00e1 purpura. Ta se zpo\u010d\u00e1tku m\u016f\u017ee projevovat jen zv\u00fd\u0161enou tvorbou mod\u0159in, krv\u00e1cen\u00edm z nosu nebo d\u00e1sn\u00ed. Projevy onemocn\u011bn\u00ed jsou zap\u0159\u00ed\u010din\u011bn\u00e9 reakc\u00ed imunitn\u00edho syst\u00e9mu, kter\u00fd postupn\u011b ni\u010d\u00ed krevn\u00ed desti\u010dky, co\u017e m\u00e1 za n\u00e1sledek zv\u00fd\u0161en\u00e9 riziko krv\u00e1cen\u00ed.2\" \/>\n<meta property=\"og:url\" content=\"https:\/\/havas.cz\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/\" \/>\n<meta property=\"og:site_name\" content=\"Havas Prague\" \/>\n<meta property=\"article:modified_time\" content=\"2020-10-14T08:20:09+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"5 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/havas.cz\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/\",\"url\":\"https:\/\/havas.cz\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/\",\"name\":\"Imunitn\u00ed trombocytopenick\u00e1 purpura je nen\u00e1padn\u00e9, ale zr\u00e1dn\u00e9 hematologick\u00e9 onemocn\u011bn\u00ed - Havas Prague\",\"isPartOf\":{\"@id\":\"https:\/\/havas.cz\/#website\"},\"datePublished\":\"2020-02-20T13:13:54+00:00\",\"dateModified\":\"2020-10-14T08:20:09+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/havas.cz\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/#breadcrumb\"},\"inLanguage\":\"en-US\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/havas.cz\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/havas.cz\/pressroom\/imunitni-trombocytopenicka-purpura-je-nenapadne-ale-zradne-hematologicke-onemocneni\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Dom\u016f\",\"item\":\"https:\/\/havas.cz\/en\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Pressroom\",\"item\":\"https:\/\/havas.cz\/pressroom\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Imunitn\u00ed trombocytopenick\u00e1 purpura je nen\u00e1padn\u00e9, ale zr\u00e1dn\u00e9 hematologick\u00e9 onemocn\u011bn\u00ed\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/havas.cz\/#website\",\"url\":\"https:\/\/havas.cz\/\",\"name\":\"Havas Prague\",\"description\":\"Agentura Havas Prague. 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